Therapy of autoinflammatory diseases: results from an international registry
نویسندگان
چکیده
Methods A web-based registry collecting baseline and clinical information of autoinflammatory diseases was located at the member area of the PRINTO website (www.printo. it). Participating hospitals included pediatric rheumatology centers of the PRINTO network and adult centers with a specific interest in autoinflammatory diseases. Data was collected on Blau’s syndrome, Behçet’s disease, CAPS, CRMO, DIRA, FMF, MKD, NLRP12-mediated periodic fever, PAPA, PFAPA TRAPS and undefined periodic fevers. In total, 704 patients were included in this retrospective study on therapy.
منابع مشابه
Trials Organisation (PRINTO) and the Eurofever/Eurotraps Projects". Treatment of autoinflammatory diseases: results from the Eurofever Registry and a literature review. ANNALS OF THE RHEUMATIC DISEASES
Objective To evaluate the response to treatment of autoinflammatory diseases from an international registry and an up‐to‐date literature review. Methods The response to treatment was studied in a web‐based registry in which clinical information on anonymised patients with autoinflammatory diseases was collected retrospectively as part of the Eurofever initiative. Participating hos...
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